Key result
Cone reconstruction of the tricuspid valve was successfully applied to a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia, sparing her from palliative shunt physiology.
Case Report (n=1)
Cone reconstruction can be successfully applied to atypical variants of Ebstein anomaly, such as those with right ventricular apical hypoplasia, to avoid palliative shunt physiology.
May expand options in select adult Ebstein cases; leaves open larger series to confirm durability.
Cone reconstruction for tricuspid valve repair has revolutionized the surgical treatment of Ebstein anomaly. We present the case of a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia who was spared from palliative shunt physiology by our use of cone reconstruction. Compared with other techniques, cone reconstruction of the tricuspid valve more closely replicates normal valvular anatomy and function. This surgical procedure can be applied to many anatomic variations of Ebstein anomaly, as in our patient's apparently unique instance of atypical Ebstein anomaly with right ventricular apical hypoplasia.
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Reddin et al. (2016) conducted a case report in Atypical Ebstein anomaly and right ventricular apical hypoplasia (n=1). Cone reconstruction was evaluated. Cone reconstruction of the tricuspid valve was successfully applied to a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia, sparing her from palliative shunt physiology.
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