X-Linked Hereditary Retinoschisis

AN X-linked degenerative retino-choroidal disease, hereditary retinoschisis, has been identified in the last 10 years. In milder cases the disease takes the form of radial macular degeneration, but in severe cases a grey sheet-like veil is attached to the detachment in the retinal vasculature, especially in the lower temporal quadrant. In differential diagnosis, according to Ricci (1960), a dominant hereditary hyaloid-retinal degeneration (Wagner, 1938) and a recessive hereditary hyaloid-tapeto-retinal degeneration (Favre, 1958) should be borne in mind.