Leucocytoclastic vasculitis associated with acquired reactive perforating collagenosis

Reactive perforating collagenosis is a rare dermatosis, firstly described in 1967 and known to manifest as an inherited autosomal recessive form occurring in childhood and a sporadic, acquired form. There is no report of an association between perforating collagenosis and cutaneous vasculitis until now. The case presented shows the association of these two disease entities and discusses in detail histopathologic and clinical features, differential diagnoses and pathomechanisms of these entities.