Key result
Two male patients presented with noncompaction of the ventricular myocardium, demonstrating typical clinical and echocardiographic features including bicuspid aortic valve and right ventricular involvement.
Case Report (n=2)
Highlights the clinical and echocardiographic presentation of ventricular noncompaction, including its potential association with congenital anomalies like bicuspid aortic valve and right ventricular involvement.
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Does not alter management; leaves open need for studies on noncompaction associations with bicuspid aortic valve and right ventricular involvement.
Noncompaction of the ventricular myocardium is a rare, unclassified cardiomyopathy due to an arrest of myocardial morphogenesis. The characteristic echocardiographic findings consist of multiple, prominent myocardial trabeculations and deep intertrabecular spaces communicating with the left ventricular (LV) cavity. The disease typically involves the LV myocardium, but right ventricular (RV) involvement is not uncommon. The clinical manifestations include heart failure (HF) signs, ventricular arrhythmias and cardioembolic events. Noncompacted myocardium may occur as an isolated cardiac lesion, as well as it can be in association with congenital anomalies. We describe two illustrative cases of noncompaction of the ventricular myocardium, a 19-year-old male with bicuspid aortic valve and progressive worsening of HF, and a 61-year-old male with marked RV involvement in addition to LV apical involvement, both with the typical clinical and echocardiographic features of the disease.
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Çavuşoğlu et al. (2003) conducted a case report in Noncompaction of the ventricular myocardium (n=2). Noncompaction of the ventricular myocardium was evaluated. Two male patients presented with noncompaction of the ventricular myocardium, demonstrating typical clinical and echocardiographic features including bicuspid aortic valve and right ventricular involvement.
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