This case report describes a previously undocumented congenital heart defect complex involving mixed levocardia, aortic atresia, and absent tricuspid valve.
Alerts clinicians to a novel CHD complex; extends anatomic spectrum but leaves management implications open.
Clinical, angiographic and pathologic features are described in a 36-hour-old male infant with mixed (discordant) levocardia, aortic valve atresia, absent tricuspid (left atrioventricular) valve and resultant massive cardiomegaly. This is the first reported case of this type of complex in a heart with discordant chambers. A possible embryologic explanation is offered for the concomitant presence of semilunar valve atresia and absence of the tricuspid valve.
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Brenner et al. (1978) studied this question.
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