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This case report demonstrates a rare late presentation of arrhythmogenic right ventricular cardiomyopathy at age 60, successfully managed with amiodarone.
Arrhythmogenic cardiomyopathy (ACM) is a progressive genetic disease of the myocardium characterized by loss of myocardial cells and replacement by fibrofatty tissue in the right and/or left ventricle (RV/LV), clinically manifested by syncope, palpitations, heart failure, or sudden cardiac death (SCD). We presented a case where the patient suffered from palpitations for the previous three to four years, which resolved spontaneously each time and lately presented with persistent palpitations and chest discomfort. ECG showed a widening of the QRS complexes during sinus rhythm and premature complexes (PVCs) of various patterns. After initial evaluation cardiac MRI was done which revealed typical features of arrhythmogenic right ventricular dysplasia/ cardiomyopathy. The patient was continuing amiodarone 100 mg daily and doing well.
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Das et al. (2023) studied this question.
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