Embryonal rhabdomyosarcoma (sarcoma botryoides) of the biliary tree.Report of five cases and a review of the literature

Clinicopathologic features of 5 embryonal rhabdomyosarcomas of the biliary tree are reported and compared with 18 examples from the literature. Embryonal rhabdomyosarcoma of the biliary tree is a rare lesion but must be considered in the differential diagnosis of jaundice in childhood. In their gross and histologic characteristics and natural history, these tumors resemble embryonal rhabdomyosarcoma in other locations. Chemotherapy and irradiation may decrease the size of the tumor, but any hope for cure appears to lie with radical surgery.