Neurofibromatosis type-1 (NF1) is a genetic disorder characterized by café-au-lait spots, neurofibroma and other associated features. The risk of malignancy is approximately 2.5 to 4-fold higher as compared to general population. However, primary pulmonary sarcoma is rarely reported in patients with NF1. Here, we describe a case of NF1 complicated with primary pulmonary sarcoma.
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Boo et al. (2014) studied this question.
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