Population
Zebrafish embryos (accordion (acc)(dta5) mutants)
Comparison
Mutation in atp2a1/SERCA1 vs Other acc alleles (recessive)
Design
Preclinical
Authors
Loading...
Supports acc(dta5) zebrafish as sensitive Brody disease model; leaves open human translation of SERCA1 mechanisms.
The acc(dta5) zebrafish mutant harbors a dominant mutation in atp2a1/SERCA1, providing a sensitive model for Brody disease, an exercise-induced impairment of muscle relaxation.
Olson et al. (2010) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: