Extramammary paget's disease-epidermotrophic carcinoma of the anal region

Summary and Conclusions This is the fifteenth case of perianal extramammary Paget's disease reported in medical literature (Table 1). Diagnosis by early biopsy, or repeated biopsies, and histochemical study of the tissues removed is necessary for accurate diagnosis. Treatment consists of wide local excision with follow-up biopsy examinations. Metastasis may be local or widespread.