Hereditary Hemorrhagic Telangiectasia: A Report of Pulmonary Arteriovenous Fistulae in Mother and Son; Medical (Hormonal) and Surgical Therapy of This Disease

Case Reports1 November 1954HEREDITARY HEMORRHAGIC TELANGIECTASIA: A REPORT OF PULMONARY ARTERIOVENOUS FISTULAE IN MOTHER AND SON; MEDICAL (HORMONAL) AND SURGICAL THERAPY OF THIS DISEASEEDWARD C. HEYDE, M.D.EDWARD C. HEYDE, M.D.Search for more papers by this authorAuthor, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-41-5-1042 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptHereditary hemorrhagic telangiectasia is one form of capillary heredopathia distinguished by the familial incidence of dilated small blood vessels histologically comprising a single layer of endothelium, with a conspicuous deficiency of muscular and elastic layers of the vessel walls.1The lesions are true vascular "spiders," such as one sees in pregnancy2and in acute or chronic liver disease. They occur most commonly on the oral and nasal mucosa, lips, face, arms and upper trunk, but may also be located in the viscera or, indeed, anywhere in the body. The association of pulmonary arteriovenous aneurysms (fistulae) with this disease has been...Bibliography1. SingerWolfson KWQ: Hemorrhagic telangiectasis; analysis of capillary heredopathies, New England J. Med. 230: 637-642, 1944. CrossrefGoogle Scholar2. BeanCogswellDexterEmbick WBRMJF: Vascular changes of the skin in pregnancy: vascular spiders and palmar erythema, Surg., Gynec. and Obst. 88: 739, 1949. MedlineGoogle Scholar3. Symposium: Congenital familial hemorrhagic telangiectases (Clinical conference, Brooke General Hospital), Bull. U. S. Army M. Dept. 8: 613-628 (Aug.) 1948. MedlineGoogle Scholar4. MoyerAckerman JHAJ: Hereditary hemorrhagic telangiectases associated with pulmonary arteriovenous fistula in two members of a family, Ann. Int. Med. 29: 775-802 (Nov.) 1948. LinkGoogle Scholar5. ArmentroutUnderwood HLFJ: Familial hereditary hemorrhagic telangiectasia with associated pulmonary arteriovenous aneurysm, Am. J. Med. 7: 246 (Feb.) 1950. CrossrefGoogle Scholar6. IsraelGosfield HLE: Fatal hemoptysis from pulmonary arteriovenous fistula: report of a case in a patient with hereditary hemorrhagic telangiectasia, J. A. M. A. 152: 40 (May 2) 1953. CrossrefMedlineGoogle Scholar7. TobinWilder JRTC: Pulmonary A-V fistula associated with hereditary hemorrhagic telangiectasia: report of occurrence in father and son, Ann. Int. Med. 38: 868 (Apr.) 1953. LinkGoogle Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: Vancouver, Washington*Received for publication December 28, 1953. PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited byGastrointestinal bleeding, angiodysplasia, cardiovascular disease, and acquired von Willebrand syndromePharmacologic Therapy of Arteriovenous MalformationsIntrapleural rupture of a pulmonary arteriovenous fistula occurring just beneath the pleura: Report of a caseGenetics of Steroid Receptors and Their DisordersSpontaneous haemothorax in Osler-Weber-Rendu disease.Hemorrhage Associated with TelangiectasesHemotorax como complicacion de una fistula arteriovenosa pulmonarOsler's Disease With Multiple Large Vessel AneurysmsIntrapleural Rupture of Pulmonary Arteriovenous AneurysmKurzschlußverbindungen des großen und kleinen KreislaufsHereditary Hemorrhagic Telangiectasia and Gastrointestinal HemorrhagePulmonary arteriovenous fistulasMultiple Small Pulmonary Arteriovenous FistulasThe Clinical Significance of Hereditary Hemorrhagic TelangiectasiaHereditary Hemorrhagic Telangiectasia and Pulmonary Arteriovenous FistulaAnomalies of the Respiratory TractSuccessful Resections for Bilateral Pulmonary Arteriovenous FistulasHereditary Hemorrhagic Telangiectasis*HEMORRHAGIC TELANGIECTASIA TREATED WITH STILBESTROL*JOHN V. WALLER, M.D.Pulmonary arteriovenous fistulaCurrent pediatric references 1 November 1954Volume 41, Issue 5Page: 1042-1053KeywordsAneurysmsBlood vesselsCapillariesChronic liver diseaseEndotheliumGenetic diseasesHormonal therapyLesionsNasal mucosaPulmonary diseases ePublished: 1 December 2008 Issue Published: 1 November 1954 PDF downloadLoading ...