Case report demonstrates Papillon–Lefèvre syndrome presenting with severe periodontal destruction in an 11-year-old girl, highlighting the need for early multidisciplinary intervention.
Papillon–Lefèvre syndrome is a rare autosomal recessive disorder characterized by palmoplantar keratoderma and aggressive periodontitis. We report an 11‐year‐old Nepalese girl presenting with severe periodontal destruction and characteristic cutaneous manifestations. Clinical and radiographic findings established the diagnosis. Early multidisciplinary management is essential to preserve function and improve quality of life.
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Bhattarai et al. (2026) studied this question.
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