Key result
Implantation of a single-chamber automated implantable cardioverter-defibrillator successfully prevented ventricular tachyarrhythmias over a 6-month follow-up in a 3-year-old boy with LQT3 syndrome.
Why the study?
This report highlights how the diagnosis of LQT3 was arrived at in the absence of readily available genetic testing, along with the anesthetic challenges in managing LQTS.
Case Report (n=1)
No
This case highlights the clinical diagnostic approach for LQT3 in the absence of genetic testing and the anesthetic challenges during AICD implantation in a pediatric patient.
A diagnosis of congenital long QT interval syndrome based on history and electrocardiogram was made in a child in the absence of readily available genetic testing. A genotype 3 (LQT3) was suspected after exclusion of other variants as the child was non-responsive to beta-blocker and sodium channel blocker medication. As the child continues to show episodic bradycardia, polymorphic ventricular ectopy, and T-wave alternans, a single-chamber automated implantable cardioverter-defibrillator implantation was done successfully. This report highlights how the diagnosis of LQT3 was arrived at as well as the anesthetic challenges in the management of patients with LQTS.
No takes yet. Share an insight, caveat, or question.
Maddali et al. (2022) conducted a case report in Type 3 Long QT (LQT3) Syndrome (n=1). Automated implantable cardioverter defibrillator (AICD) was evaluated on Arrhythmia recurrence and device shocks. Implantation of a single-chamber automated implantable cardioverter-defibrillator successfully prevented ventricular tachyarrhythmias over a 6-month follow-up in a 3-year-old boy with LQT3 syndrome.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: