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November 1, 2015Indian Pacing and Electrophysiology JournalOpen Access

Genetic screening of 46 Long QT Syndrome families identified novel variations and compound heterozygosity in 18 probands (39.1%), highlighting the role of cardiac genes in a recessive fashion.

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Population

46 families with Long QT Syndrome (LQTS), including symptomatic and asymptomatic family members and probands

Design

Cohort

Key result

Genetic screening of 46 Long QT Syndrome families identified novel variations and compound heterozygosity in 18 probands (39.1%), highlighting the role of cardiac genes in a recessive fashion.

Authors

SQSameera Fatima QureshiAAAltaf AliVAVenkateshwari Ananthapur

Discussion

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Overview

May support LQTS family screening for risk stratification; leaves open recessive inheritance effects pending prospective validation.

Study Design

Type

Observational (n=46)

Structured PICO

P
Population
46 families of Long QT Syndrome probands undergoing genetic screening to identify genotype-phenotype correlations.
E
Exposure
Genetic testing and screening of family members
O
Outcome
Identification of genetic variations and genotype-phenotype correlationssurrogate

Genetic screening of LQTS families identifies novel variations and compound heterozygosity, aiding in risk stratification and predictive testing for first-degree relatives.

Cite This Study

Qureshi et al. (2015) conducted an observational in Long QT Syndrome (LQTS) (n=46). Genetic screening was evaluated on Novel variations or compound heterozygosity in screened genes. Genetic screening of 46 Long QT Syndrome families identified novel variations and compound heterozygosity in 18 probands (39.1%), highlighting the role of cardiac genes in a recessive fashion.

synapsesocial.com/papers/6a984f7b329299b5dce34fb0https://doi.org/10.1016/j.ipej.2015.12.001
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Also Consider

Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context:

  1. 1Clinical Heterogeneity in Patients with Long QT Syndrome and Segregation of Single Nucleotide Variants and Clinical Symptoms in 17 Affected Families2023 · 2 citations
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  3. 3Clinical and Genetic Characteristics of 18 Cases with Suspected Congenital Long QT Syndrome: A Retrospective Cross-Sectional Study2024 · 2 citations
  4. 4Allelic Complexity in Long QT Syndrome: A Family-Case Study2017 · 11 citations
  5. 5Gene-Targeted Analysis of Clinically Diagnosed Long QT Russian Families2016 · 22 citations