Answers are grounded in this paper and cite their sources.
Vasculopathy is a relatively frequent but poorly recognised manifestation of von Recklinghausen's neurofibromatosis. One of its more dramatic presentations is as spontaneous haemothorax. Clinicians and pathologists should be aware of this syndrome as a cause of sudden death in patients with neurofibromatosis.
No takes yet. Share an insight, caveat, or question.
Griffiths et al. (1998) studied this question.
Synapse has enriched 10 related papers. Consider them for comparative context: