Key result
Congenital triple valve stenosis sparing the aortic valve presented at age 51 with shortness of breath and central cyanosis, without demonstrable intracardiac right-to-left communication.
This case report describes a rare presentation of congenital triple valve stenosis with dominant pulmonary valve disease in a 51-year-old patient.
Rare adult presentation of congenital triple valve stenosis warrants inclusion in cyanosis differentials; leaves open questions on natural history and management.
We report a case of congenital triple valve stenosis with dominant pulmonary valve disease, sparing the aortic valve, presenting at the age of 51 years with progressive shortness of breath and central cyanosis. At post mortem, no intracardiac right to left communication could be demonstrated.
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Besouw et al. (1983) studied this question. Congenital triple valve stenosis sparing the aortic valve presented at age 51 with shortness of breath and central cyanosis, without demonstrable intracardiac right-to-left communication.
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