Wegener’s Granulomatosis: An Unusual PresentationCase Report and Review of Literature

Wegener’s granulomatosis is a rare vasculitic disorder affecting multiple systems and typically involves the kidneys, lungs and the nose. Its presentation as an isolated involvement of the ear is very uncommon and only a few cases presenting as an isolated involvement of the ear with unilateral facial palsy and deafness have been reported in world literature. We report a case of isolated otological involvement presenting as facial palsy and bilateral profound deafness. The renal and pulmonary systems and the nose were unaffected.