Key result
Surgical correction of adult ALCAPA with AF maintains sinus rhythm and stability at 3 years.
Why the study?
ALCAPA is a rare congenital coronary anomaly with diverse presentations, and initial presentation with AF is exceptionally rare and often results in misdiagnosis.
Case Report (n=1)
No
This case highlights that adult-type ALCAPA can rarely present initially with atrial fibrillation and can be successfully managed with a comprehensive surgical strategy including coronary reimplantation, valve surgery, and arrhythmia ablation.
AF as rare ALCAPA presentation warrants diagnostic vigilance in select cases; leaves open whether broader screening improves outcomes.
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital coronary anomaly characterized by diverse clinical presentations. Atrial fibrillation (AF) as the initial presentation is exceptionally rare and often results in misdiagnosis. This report describes a rare case of adult-type ALCAPA manifesting initially as AF, detailing a comprehensive surgical strategy and long-term outcomes.
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He et al. (2026) conducted a case report in Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) presenting with atrial fibrillation (n=1). Comprehensive surgical correction (LCA reimplantation, mechanical MVR, tricuspid annuloplasty, LAA ligation, modified maze procedure) was evaluated on Clinical stability and rhythm maintenance. Comprehensive surgical correction of adult-type ALCAPA presenting with atrial fibrillation resulted in sustained sinus rhythm and clinical stability at 3-year follow-up.
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