Visceral Changes in Myotonic Dystrophy

Article1 November 1965Visceral Changes in Myotonic DystrophyBERNARD M. SCHUMAN, M.D., JOSEPH A. RINALDO JR., M.D., J. DANA DARNLEY, M.D.BERNARD M. SCHUMAN, M.D., JOSEPH A. RINALDO JR., M.D., J. DANA DARNLEY, M.D.Author, Article, and Disclosure Informationhttps://doi.org/10.7326/0003-4819-63-5-793 SectionsAboutPDF ToolsAdd to favoritesDownload CitationsTrack CitationsPermissions ShareFacebookTwitterLinkedInRedditEmail ExcerptThe myotonia and eventual atrophy of skeletal muscle have diverted attention from alterations of other muscular structures in myotonic dystrophy. In recent years greater recognition of this disease as a generalized muscular disorder has come about because of reports of significant cardiopulmonary changes (1). These changes have been found prior to clinically evident skeletal myotonia in some instances (2). That smooth muscle may be affected has not been widely appreciated, and associated functional alteration of viscera has been overlooked as a source of symptoms in this disorder.METHODSWe studied seven males and five females who had clinical evidence of...References1. KILBURNEAGANSIEKERHEYMAN KHJTHOA: Cardiopulmonary insufficiency in myotonic and progressive muscular dystrophy. New Eng. J. Med. 261: 1089, 1959. CrossrefMedlineGoogle Scholar2. CANNON PJ: The heart and lungs in myotonic muscular dystrophy. Amer. J. Med. 32: 765, 1962. CrossrefMedlineGoogle Scholar3. RINALDOGAHAGAN JAT: Narrow lower esophageal ring. Pathogenesis and physiology. Amer. J. Dig. Diseases. In press. Google Scholar4. SIEGEL S: Nonparametric Statistics for the Behavioral Sciences. McGraw-Hill Book Co., Inc. New York, 1956. p. 116. Google Scholar5. KRAMERATKINSONWYMANINGELFINGER PMSMFJ: The dynamics of swallowing: II, neuromuscular dysphagia of the pharynx. J. Clin. Invest. 36: 589, 1957. 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Thorax 9: 67, 1954. CrossrefMedlineGoogle Scholar26. CAUGHEYPACHOMOV JEN: The diaphragm in dystrophia myotonica. J. Neurol. Neurosurg. Psychiat. 22: 311, 1959. CrossrefMedlineGoogle Scholar This content is PDF only. To continue reading please click on the PDF icon. Author, Article, and Disclosure InformationAffiliations: Detroit, MichiganFrom the Division of Gastroenterology, Henry Ford Hospital, Detroit, Mich.Requests for reprints should be addressed to Bernard M. Schuman, M.D., Associate Physician, Division of Gastroenterology, Henry Ford Hospital, Detroit, Mich. 48202. PreviousarticleNextarticle Advertisement FiguresReferencesRelatedDetails Metrics Cited ByIs there a difference in gastric emptying between myotonic dystrophy type 1 patients with and without gastrointestinal symptoms?Esophageal Manifestations of Collagen Vascular and Other Systemic DiseasesGastrointestinal manifestations in myotonic muscular dystrophyGastric emptying in myotonic dystrophyGastric emptying in myotonic dystrophic patientsIntestinal non-rotation and pseudoobstruction in myotonic dystrophy: case report and review of the literatureGastrointestinal Symptoms in Myotonic DystrophySwallowing problems in neuromuscular disordersCase report: Selective occipital lobe hydrocephalus and agenesis of the left lobe of the liver in congenital myotonic dystrophyAnal abnormalities in childhood myotonic dystrophy--a possible source of confusion in child sexual abuse.The effects of cisapride on gastric and oesophageal emptying in dystrophia myotonicaGastric and esophageal emptying in dystrophia myotonicaEsophageal Motor Function in Patients With Muscular DystrophyDerangement of swallowing in children with myelomeningoceleFunctional Abnormalities of the Anal Sphincters in Patients With Myotonic DystrophyGastrointestinal manifestations of the muscular dystrophiesPharyngoesophageal motor function in patients with myotonic dystrophyGastroduodenal motility in a case of dystrophia myotonicaMyotonic dystrophy associated with thyroid diseaseSmooth muscle in an animal model of myotonic dystrophyAltered tracheal smooth muscle activities in an animal model of human myotonic dystrophyINTESTINAL ABSORPTION IN MYOTONIC DYSTROPHYLes formes néo-natales de la dystrophie myotonique de steinertMotor Disorders Due to Muscle DisordersEsophageal and Colon Changes in Myotonia DystrophicaGastric bezoar in a patient with myotonic dystrophyThe radiologic features of myotonic dystrophy with presentation of a new findingHereditäre MyopathienON THE METABOLISM OF HISTAMINE IN DYSTROPHIA MYOTONICAProgress in Gastroenterological Radiology 1 November 1965Volume 63, Issue 5Page: 793-799KeywordsAtrophyDysphagiaElectrocardiographyEsophagusMuscular diseasesMyotonic dystrophySkeletal musclesSmooth muscles Issue Published: 1 November 1965 PDF DownloadLoading ...