Complete failure of eruption of all permanent teeth: An autosomal dominant disorder

A disorder is described which involves persistent deciduous teeth and complete lack of eruption of the permanent teeth. An anomaly of the jaw bones leading to impaction of all the permanent teeth seems to be responsible for the observed manifestations. A family is presented with three affected individuals plus one other reputedly affected. The distribution of patients in the pedigree is consistent with autosomal dominant inheritance of the disorder reported.