Development of a schwannoma within a facial nerve neurofibroma: A case report and literature review

We report the presence of a schwannoma within a neurofibroma of the intratemporal facial nerve. This neurofibroma recurred 39 years after its first excision in the parotid gland. Although some believe that schwannomas and neurofibromas represent the same entity, these tumors present distinctive histopathologic and clinical characteristics, which are discussed. The extreme rarity of a schwannoma developing within a neurofibroma is underlined. This is the first report of such an association occurring within a cranial nerve.