Key result
An 11-year-old girl with STK4 deficiency developed primary cardiac T-cell lymphoma, initially responding to chemotherapy but ultimately dying from lung hemorrhage two months post-operation.
Population
11-year-old girl with primary immunodeficiency presenting with primary cardiac T-cell lymphoma.
Design
Case_report
Follow-up
2 months after operation
Authors
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Raises possibility of cardiac lymphoma in STK4 deficiency; extends malignancy associations but remains hypothesis-generating.
Case Report (n=1)
This first reported case of primary cardiac T-cell lymphoma in a patient with STK4 deficiency highlights the need to consider this rare malignancy in immunodeficient patients presenting with intracardiac masses.
Sherkat et al. (2017) conducted a case report in Primary cardiac T-cell lymphoma in STK4 deficiency (n=1). Chemotherapy and emergency debulking surgery was evaluated on Clinical outcome. An 11-year-old girl with STK4 deficiency developed primary cardiac T-cell lymphoma, initially responding to chemotherapy but ultimately dying from lung hemorrhage two months post-operation.
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