Key result
Doty's two-sinus aortoplasty shows excellent outcomes for supravalvular aortic stenosis in a Williams syndrome case.
Case Report (n=1)
Doty's method of extended aortoplasty (two sinus reconstructions) is a successful surgical approach for treating congenital supravalvular aortic stenosis in patients with Williams's syndrome.
May support Doty's aortoplasty in select Williams syndrome cases; leaves open durability and generalizability.
We experienced a successful surgical Williams's syndrome case of extended aortoplasty by means of Doty's method (two sinus reconstructions) for congenital supravalvular aortic stenosis. Case was 29-year-old woman, who had no complaint except heart murmur and dyspnea. The retrograde aortography and Digital Subtraction Angiography (DSA) demonstrated localized stenosis just above the aortic valve, and it was an hour-glass type. This case showed excellent results. Doty's aortoplasty was favorable method for supravalvular aortic stenosis without deformity of aortic valve and coronary obstruction.
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Tiryakioğlu et al. (2009) conducted a case report in Williams's syndrome with congenital supravalvular aortic stenosis (n=1). Doty's method (two sinus reconstructions) extended aortoplasty was evaluated on Surgical success / clinical outcome. Doty's aortoplasty (two sinus reconstructions) was successfully performed in a 29-year-old woman with Williams's syndrome and congenital supravalvular aortic stenosis, showing excellent results.
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