Key result
Surgery and systemic chemotherapy achieve 14-month disease stability and symptom improvement in pleural EH.
Case Report (n=1)
A rare case of pleural epithelioid hemangioendothelioma compressing the myocardium was successfully managed with surgery and chemotherapy, resulting in stable disease at 14 months.
May support surgery plus chemotherapy for symptom control in pleural EH; hypothesis-generating and should not change practice.
Epithelioid haemangioendothelioma (EH) is a rare malignant tumor of vascular origin that usually arises in bone, liver, soft tissue, or lung. EH originating in the pleura has been less frequently described. We describe an uncommon case of pleural EH compressing the myocardium in a 39-year-old woman. The patient was diagnosed with pleural EH confirmed by surgery and immunohistochemistry. She sustained stable disease 14 months after the diagnosis and her symptoms improved after systemic chemotherapy with carboplatine and etoposide. Complete surgical excision of pleural EH followed chemotherapy may prolong survival.
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Yu et al. (2013) conducted a case report in Pleural epithelioid hemangioendothelioma compressing the myocardium (n=1). Surgery and systemic chemotherapy (carboplatine and etoposide) was evaluated on Stable disease and symptom improvement. Complete surgical excision followed by systemic chemotherapy with carboplatine and etoposide resulted in stable disease and symptom improvement at 14 months in a patient with pleural EH.