Frequency Selectivity and Temporal Processing in Friedreich's Ataxia

We performed psychoacoustical tuning curves and measured temporal summation in two patients with Friedreich's ataxia to study aspects of frequency selectivity and temporal processing in the auditory system. In the majority of frequencies tested, normal psychoacoustical tuning curves and unimpaired temporal summation functions were obtained. These findings suggest that the processing mechanism responsible for these phenomena is intact.