A 30 year old man with von Hippel-Lindau syndrome presented with obstructive jaundice caused by a carcinoid tumour of the mid- and upper common bile duct. This association is probably causally related in view of the propensity for patients with von Hippel-Lindau syndrome to develop neuroendocrine tumours.
No takes yet. Share an insight, caveat, or question.
Fellows et al. (1990) studied this question.
Synapse has enriched 5 related papers. Consider them for comparative context: