Key result
Rare Marfan syndrome case features an aortic dissection starting distal to the left subclavian artery.
Why the study?
Marfan syndrome commonly causes aortic root dilation and dissection beginning above the coronary ostia, but dissection distal to the left subclavian artery is rare.
Case Report (n=1)
No
Highlights a rare presentation of aortic dissection in Marfan syndrome originating in the descending aorta rather than the typical ascending aorta.
Atypical descending aortic dissection possible in Marfan syndrome; leaves open whether surveillance protocols need revision.
Marfan syndrome is an inheritable connective tissue disorder with protean clinical manifestations involving the ocular, skeletal and cardiovascular system. It is well estabalished that the major cause of morbidity in Marfan syndrome is the dilation of the aortic root as well as the associated aortic regurgitation and dissection. Aortic dissection usually begins just above the coronary ostia in the ascending aorta and extends the entire length of aorta. We report a rare case of Marfan syndrome with aortic dissection which begins distal to the left subclavian artery in the descending aorta.
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Oh et al. (1998) conducted a case report in Marfan syndrome with dissecting aortic aneurysm (n=1). Marfan syndrome with aortic dissection was evaluated. A rare case of Marfan syndrome was reported featuring an aortic dissection that begins distal to the left subclavian artery in the descending aorta.
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