Key result
Supportive management and regular outpatient follow-up describe care for two children with restrictive cardiomyopathy.
Why the study?
Restrictive cardiomyopathy is one of the rarest forms of cardiomyopathies in paediatric patients, and no cases had yet been reported from Oman.
Case Report (n=2)
No
This case series highlights the clinical presentation and supportive management of rare paediatric restrictive cardiomyopathy in Oman.
Answers are grounded in this paper and cite their sources.
May inform supportive care in rare paediatric restrictive cardiomyopathy; leaves open need for larger regional registries and prospective studies.
Restrictive cardiomyopathy is one of the rarest forms of cardiomyopathies in paediatric patients characterised by impaired myocardial relaxation or compliance with restricted ventricular filling, leading to a reduced diastolic volume with a preserved systolic function. We report 2 cases—a 5-year-old boy who presented with abdominal distension and palpitation with family history of similar complaints but no definite genetic diagnosis as yet and a 5-year-old girl who presented with chronic cough and shortness of breath. Both cases were diagnosed in a tertiary care hospital in Muscat, Oman, in 2019 and are managed supportively with regular outpatient follow-up. This is the first series of reported cases of paediatric restrictive cardiomyopathy from Oman.
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Senaidi et al. (2023) conducted a case report in Paediatric Restrictive Cardiomyopathy (n=2). Supportive management was evaluated. Two 5-year-old children diagnosed with restrictive cardiomyopathy in Oman were managed supportively with regular outpatient follow-up.
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