Key result
Isolated right inferior pulmonary vein stenosis presents asymptomatically with chronic venous collateral compensation and mild PH.
Why the study?
Asymptomatic primary isolated pulmonary vein stenosis in adults with chronic compensation and mild pulmonary hypertension is rarely reported.
Case Report (n=1)
This case demonstrates that primary isolated pulmonary vein stenosis can remain asymptomatic in adults due to chronic compensation by venous collateral circulation.
Isolated pulmonary vein stenosis may remain asymptomatic via collaterals; leaves open questions on prevalence and surveillance in adults.
A 31-year-old man without respiratory symptoms was transferred to our clinic with incidentally detected small nodular densities in both the upper lung zones on chest radiography. Chest computed tomography and pulmonary angiography demonstrated that the entrance of the right inferior pulmonary vein to the left atrium was completely blocked, and the venous return of the right lower lobe was achieved through the right superior pulmonary vein with a tortuous venous collateral complex in the venous phase. With echocardiography, mild pulmonary hypertension was detected. Here, we present an asymptomatic adult with isolated stenosis of the pulmonary vein with chronic compensation by venous collateral circulation in spite of mild pulmonary hypertension.
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Kim et al. (2010) conducted a case report in Primary isolated pulmonary vein stenosis (n=1). Primary isolated pulmonary vein stenosis was evaluated. A 31-year-old asymptomatic man was found to have isolated stenosis of the right inferior pulmonary vein with chronic compensation by venous collateral circulation and mild pulmonary hypertension.
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