Key result
Surgery successfully treats a large septal fibroma causing simultaneous biventricular outflow tract obstruction.
Case Report (n=1)
No
This case report describes a rare presentation of a cardiac fibroma causing simultaneous bilateral ventricular outflow tract obstruction in an infant, successfully diagnosed with MRI and treated surgically.
Septal fibroma can cause simultaneous biventricular outflow obstruction in infants; extends phenotypic spectrum of cardiac tumors but leaves optimal management open.
Heart fibroma accounts for about 5% of all primary neoplasms and is registered in children in 80% of cases. The ventricles or interventricular septum (IVS) are most often affected; in half of cases, the tumor has intracavitary growth. The clinical picture of the disease and its prognosis depend on the size and location of the tumor. The most unfavorable is the defeat of the IVS, since it causes obstruction of the output tract of one of the ventricles. Being localized in IVS, can involve a conducting system of heart, thereby increasing risk of sudden death. A retrospective study of a case of cardiac fibroma in a child aged 4.5 months, confirmed by echocardiography, magnetic resonance imaging and successfully operated on in the Central Federal District Center of Penza, is presented. A large tumor, localized in the IVS, caused atypical obstruction of the outflow tracts of both ventricles simultaneously. In the domestic and foreign literature, hemodynamic disturbances of only one of the ventricles are described, and we did not find a single case with simultaneous obstruction of both tracts. The possibility of MRI in the diagnosis of heart tumors has been shown.
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Карпухин et al. (2021) conducted a case report in Cardiac fibroma (n=1). Surgical treatment was evaluated. A large cardiac fibroma in the interventricular septum of a 4.5-month-old child caused atypical simultaneous obstruction of both ventricular outflow tracts and was successfully treated with surgery.
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