Key result
Cardiac inflammatory myofibroblastic tumors in young patients link to ~10% sudden death from prolapse or embolization.
Why the study?
Cardiac tumors other than myxomas are rare and their clinical features, outcomes, and distinctions from other cardiac tumors are not well characterized.
Population
10 children and young adults with intracavitary polypoid myofibroblastic proliferations
Comparison
Surgical resection, cardiac transplant, or autopsy diagnosis
Design
Case series
Follow-up
Long-term follow-up in 2 patients
Authors
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May warrant suspicion for these tumors in young patients with unexplained syncope or arrest; leaves open natural history and management.
Case Report (n=10)
Cardiac inflammatory myofibroblastic tumors are rare, histologically benign neoplasms that can cause severe, life-threatening clinical events such as myocardial infarction and sudden death due to their intracavitary location.
Burke et al. (2007) conducted a case report in Cardiac inflammatory myofibroblastic tumor (n=10). Cardiac inflammatory myofibroblastic tumor was evaluated. Cardiac inflammatory myofibroblastic tumors in 10 young patients caused serious complications including shortness of breath (30%), syncope (20%), and sudden death (10%) due to prolapse or embolization.
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