Key result
Transcatheter ASD closure yields clinical stability through 3 years in a patient with ARVC.
Why the study?
Arrhythmogenic right ventricular cardiomyopathy associated with atrial septal defect is very rare and complicates diagnosis, treatment, and prognosis.
Case Report (n=1)
Transcatheter closure of an atrial septal defect in a patient with arrhythmogenic right ventricular cardiomyopathy was feasible and associated with clinical stability over 3 years.
Transcatheter ASD closure feasible in rare ARVC association; leaves open long-term outcomes and arrhythmia management strategies.
Arrhythmogenic right ventricular cardiomyopathy is characterised by progressive, fibrofatty replacement of myocardium, and ventricular arrhythmias, and its prognosis is usually poor. Arrhythmogenic right ventricular cardiomyopathy associated with atrial septal defect is very rare, and this combination may make the diagnosis, treatment, and prognosis difficult. We present a case of a patient with this association who underwent interventional treatment with a septal defect occluder. Transcatheter closure of atrial septal defect in a patient with arrhythmogenic right ventricular cardiomyopathy is hitherto unreported. During a 3-year follow-up he remained relatively stable. We also review the cases reported in the medical literature describing this uncommon association between arrhythmogenic right ventricular cardiomyopathy and atrial septal defect or patent foramen ovale.
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Wang et al. (2014) conducted a case report in Arrhythmogenic right ventricular cardiomyopathy associated with atrial septal defect (n=1). Transcatheter closure with a septal defect occluder was evaluated on Clinical stability. Transcatheter closure of an atrial septal defect in a patient with arrhythmogenic right ventricular cardiomyopathy resulted in the patient remaining relatively stable during a 3-year follow-up.
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