Key result
Multimodality 2D, 3D, and transesophageal echocardiography effectively detects and quantifies severe pulmonary supravalvular stenosis.
Why the study?
Isolated supravalvular pulmonary stenosis is a rare echocardiographic finding, especially in adults, with limited clinical descriptions available.
Case Report (n=1)
Transthoracic and transesophageal echocardiography are useful modalities for detecting and quantifying rare isolated supravalvular pulmonary stenosis in adults.
Answers are grounded in this paper and cite their sources.
Severe supravalvular PS may lack symptoms or right-heart remodeling in adults; leaves open natural history and management thresholds.
Isolated supravalvular pulmonary stenosis is a rare finding, usually evidenced in the pediatric age. Here, we report a case of a 76-year-old patient with isolated, severely obstructive, pulmonary supravalvular stenosis. The peculiarity of the present case is the paucity of symptoms and lack of changes in right heart sections, despite of the importance of stenosis. The report confirms the utility of transthoracic two- and three-dimensional echocardiography and transesophageal echocardiography in the detection and quantification of this rare anomaly.
No takes yet. Share an insight, caveat, or question.
Maffè et al. (2014) conducted a case report in Isolated supravalvular pulmonary stenosis (n=1). Transthoracic two- and three-dimensional echocardiography and transesophageal echocardiography was evaluated on Detection and quantification of the anomaly. Transthoracic two- and three-dimensional echocardiography and transesophageal echocardiography successfully detected and quantified isolated, severely obstructive pulmonary supravalvular stenosis.
Synapse has enriched 10 related papers. Consider them for comparative context: