Angioimmunoblastic lymphadenopathy: A case with an unusual clinical course with marked tumorous infiltration of multiple organs and striking intestinal involvement

An unusual case of angioimmunoblastic lymphadenopathy (AILD) with a rare clinical course and marked gastrointestinal involvement is reported. Two years after the onset of AILD, there was a dramatic alteration in the clinical picture which appeared to take on a malignant course. Despite the clinical course and the presence of macroscopic tumors in multiple sites at autopsy, there was no transformation to immunoblastic sarcoma. The typical histologic picture of AILD was still evident in all organs examined. The rarity of massive gastrointestinal involvement in AILD is stressed.