Multimodalities Imaging of Immunoglobulin 4-related Cardiovascular Disorders

Figures

• 

  Fig. (1). CT coronary angiogram (multiplanar reformatting image, MPR) image shows diffuse encasement of the aorta and mild proximal right coronary artery stenosis (arrow) with encasing mildly enhancing soft tissue mass.

• 

  Fig. (2). MPR image of CT coronary angiogram encasement of the proximal aorta and left main coronary artery with soft tissue mass with no significant stenosis (arrow).

• 

  Fig. (3). Axial fused image of FDG PET-CT shows circumferential thinking of the pericardium with patchy area of FDG uptake (arrow), a finding that is consistent with mild pericardial effusion and acute pericarditis.

• 

  Fig. (4). Color flow Doppler of the pulmonary valve showed an area of systolic high-grade turbulence at the level of the pulmonary valve (small coloured insert), with a peak velocity of 3.08 meter/second and maximum pulmonary pressure gradient of 37.44 mm/HG consistent with moderate pulmonary valve stenosis.

• 

  Fig. (5). A: Coronal non-contrast enhanced CT image of the chest demonstrates diffuse circumferential thickening of the wall of the ascending thoracic aorta (arrows). B: axial T1 weighted image MR image shows severe wall thickening of the ascending thoracic aorta (arrow).

• 

  Fig. (6). Coronal fused FDG PET-CT image shows diffuse mild FDG uptake in the ascending thoracic aorta consistent with active inflammatory peri aortitis.

• 

  Fig. (7). Volume rendering image of the CT pulmonary angiogram shows severe narrowing of the proximal main and right pulmonary artery (arrows).

• 

  Fig. (8). Color Doppler ultrasound showed complete occlusion of the left internal carotid artery with the reversal of diastolic flow.