Key result
VSD and pulmonary stenosis are the most common anomalies associated with double outlet right ventricle.
Why the study?
Anatomical characteristics and associated malformations of double outlet right ventricle in children's hearts with congenital malformations were not fully described.
Observational (n=27)
This anatomical study details the morphological features and associated malformations in double outlet right ventricle, highlighting the prevalence of VSD and pulmonary stenosis.
May inform individualized DORV evaluation; leaves open generalizability to surgical outcomes in larger cohorts.
Out of 1610 children's hearts with congenital malformations there were 27 specimens showing double outlet right ventricle. Cases with dextrocardia, situs inversus, or l-venticular loop were excluded. Anatomical examination was performed with particular reference to the infundibular region, the great vessels, and the ventricular septum. The commonest associated malformations were ventricular septal defect and pulmonary stenosis. Aortic stenosis was the predominant finding in those cases dying in the neonatal period. An aortic conus was associated with pulmonary stenosis, ventricular septal defect, and d-transposition, a pulmonary conus with ventricular septal defect and a double conus with stenosis of either great vessel. The anterior vessel always had a muscular conus and the posterior vessel was commonly stenotic.
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Cameron et al. (1976) conducted an observational in Double outlet right ventricle (n=27). Double outlet right ventricle was evaluated on Anatomical findings and associated malformations. Anatomical examination of 27 double outlet right ventricle specimens revealed that ventricular septal defect and pulmonary stenosis were the most common associated malformations.