Key result
GDMT achieves NYHA class II compensation at 1 month in isolated right ventricular cardiomyopathy.
Why the study?
Idiopathic isolated right ventricular cardiomyopathy is an extremely rare cause of right ventricular failure and a diagnosis of exclusion with limited reported cases.
Case Report (n=1)
No
Answers are grounded in this paper and cite their sources.
Supports GDMT feasibility for compensated status in idiopathic isolated RV cardiomyopathy; leaves open prospective validation in larger cohorts.
Idiopathic isolated right ventricular cardiomyopathy is an extremely rare cause of right ventricular failure. Here, we report a case of 65-year-old male presented with chief complaints of dyspnea, fatigue, and bilateral pedal edema for the last 6 months. On clinical evaluation, grade II/III pansystolic murmur was present in left parasternal area. Investigations and imaging revealed dilated right atrium and ventricle with normal pulmonary artery pressure without any etiology. Magnetic resonance imaging ruled out other common causes of right ventricular cardiomyopathy; thus, the patient was diagnosed as a case of idiopathic isolated right ventricular cardiomyopathy that is a diagnosis of exclusion.
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Mohanty et al. (2023) conducted a case report in Idiopathic isolated right ventricular cardiomyopathy (n=1). Guideline-directed medical therapy was evaluated on Heart failure functional class. A 65-year-old male with idiopathic isolated right ventricular cardiomyopathy was managed with guideline-directed medical therapy, resulting in compensated heart failure in NYHA class II at one month.
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