Key result
Tailored medical or surgical therapy successfully alleviates symptoms in isolated right ventricular hypoplasia.
Why the study?
Isolated right ventricular apical hypoplasia is a rare congenital heart disease with limited reported cases and uncertain diagnostic criteria.
Case Report (n=6)
Individualized interventions may relieve symptoms in rare isolated RV hypoplasia; leaves open optimal strategies pending larger confirmatory series.
Isolated right ventricular apical hypoplasia is an unusual congenital heart disease that has been mentioned in only one report to our knowledge. We describe the case of a 62-year-old male patient suffering from recurrent abdominal distention, nausea, and lower extremity edema. The right ventricular morphologic abnormalities as shown by echocardiography and CT were comparable to those of left ventricular apical hypoplasia, suggesting right ventricular apical hypoplasia. However, this speculative diagnosis remains to be confirmed by additional cases.
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Liao et al. (2017) conducted a case report in Isolated right ventricular hypoplasia (n=6). Medical and surgical management (e.g., ASD closure, Glenn shunt) was evaluated.
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