A Rare Case of Atypical Primary Ewing’s Sarcoma of Occipital Bone

BACKGROUND ’s Sarcoma is an aggressive malignant neoplasm most frequently manifesting in the second decade of life and accounting 4% of childhood and adolescent malignancies. These tumours were first described by James Ewing in 1921 as tumours arise from bone. These osseous lesions have since become infamous for their highly aggressive course with 20% to 30% patients having evidence of metastasis at the time of diagnosis and an estimated 10-year survival rate of 50%. Metastases the CNS have most recently been estimated to occur in less than 5% of cases and are usually due to direct extension of an lesion into the extradural space or more rarely through haematogenous spread. REPORT this article, we report a case of 17-year-old boy who presented to the radiology department with complaints of recurrent of headache and vomiting for the past 3 days. On radiological investigation, there was a large well-defined, lobulated, -axial mass lesion measuring 3.6 X 5.7 X 5.9 cm noted in the supratentorial left occipital region which was fairly enhancing contrast administration. The mass was causing permeative type of destruction of the left occipital bone and extending extracranial soft tissue. Final diagnosis was done by biopsy and histopathology which showed “Atypical Ewing’s Sarcoma” the left occipital bone. Considering its unusual site and soft tissue extension, we report this case of Primary Atypical Ewing’s of occipital bone. cranial Ewing's sarcoma is to be considered in the differential diagnosis in children with a tumour involving the skull destruction of the bone and presence of extra-axial soft tissue swelling. CT is the excellent modality for demonstration of destruction while MRI depicts soft tissue extension and metastasis if any.