Surgical treatment and adjuvant chemotherapy for primary pulmonary artery chondrosarcoma were followed by tumor recurrence at 10 months and death from heart and respiratory failure at 2 years.
Case Report (n=1)
Primary pulmonary artery sarcoma is a rare condition that mimics pulmonary embolism and requires early diagnosis and treatment to prolong survival.
Background: Primary pulmonary artery sarcoma (PAS) is a rare tumor that presents like pulmonary embolism (PE), primary chondrosarcoma in the pulmonary artery is even rarer and few studies have been reported. PAS are commonly misinterpreted as in a clinical setting, many patients initially receive anticoagulant and thrombolysis therapy, but failed to respond. Management of this condition is difficult and prognosis is poor. We report a case of primary pulmonary artery chondrosarcoma that was initially misdiagnosed as PE and Inappropriate interventional therapy was performed, but with poor response. Finally, patient received surgical treatment, postoperative pathology confirmed primary pulmonary artery chondrosarcoma. Case Description: recurrence of pulmonary artery tumors in 10 months after surgery and received six cycles of adjuvant chemotherapy. The lesions progressed slowly after chemotherapy. The patient subsequently developed lung metastasis in 22 months and died of heart failure and respiratory failure 2 years after surgery. Conclusions: PAS is an extremely rare and the clinical symptoms and radiological features often mimics PE, therefore When doctors make differential diagnosis of pulmonary artery mass lesions, especially when the anticoagulation and thrombolytic effects are very poor. They need to be alert to the possibility of PAS so that early diagnosis and early treatment can prolong the survival of patients.
Zhang et al. (Sat,) conducted a case report in Primary pulmonary artery chondrosarcoma (n=1). Surgical treatment and adjuvant chemotherapy was evaluated on Clinical outcome. Surgical treatment and adjuvant chemotherapy for primary pulmonary artery chondrosarcoma were followed by tumor recurrence at 10 months and death from heart and respiratory failure at 2 years.