Desmoplakin cardiomyopathy causes arrhythmias, heart failure, and sudden cardiac death, typically presenting on cardiac MRI with ring-like subepicardial late gadolinium enhancement.
Desmoplakin cardiomyopathy is an inherited condition characterized by arrhythmias, heart failure, and sudden cardiac death, with a distinct ring-like subepicardial late gadolinium enhancement on cardiac MRI.
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Desmoplakin (DSP) cardiomyopathy is an inherited condition caused by desmosome gene DSP mutation, resulting in arrhythmias, heart failure, and sudden cardiac death. Cardiac MRI typically presents with ring-like subepicardial late gadolinium enhancement which can be mistaken for myocarditis or fatty replacement.
Han et al. (Mon,) reported a other. Desmoplakin cardiomyopathy causes arrhythmias, heart failure, and sudden cardiac death, typically presenting on cardiac MRI with ring-like subepicardial late gadolinium enhancement.