Desmoplakin cardiomyopathy is an inherited condition characterized by arrhythmias, heart failure, and sudden cardiac death, with a distinct ring-like subepicardial late gadolinium enhancement on cardiac MRI.
Desmoplakin (DSP) cardiomyopathy is an inherited condition caused by desmosome gene DSP mutation, resulting in arrhythmias, heart failure, and sudden cardiac death. Cardiac MRI typically presents with ring-like subepicardial late gadolinium enhancement which can be mistaken for myocarditis or fatty replacement.
Han et al. (Mon,) studied this question.