Congenital portosystemic shunts in children: A case series from single center

We present four children with congenital portosystemic shunts (CPSS) with varied presentation. An 8-year-old girl was incidentally detected to have CPSS during an abdominal ultrasonography. The malformation was closed using a vascular plug through femoral catheterization. A 2-month-old girl with neonatal cholestasis and a paucity of intrahepatic bile ducts on liver histopathology was detected to have CPSS. Cholestasis recovered; however, the patient was lost to follow-up. A 22-day-old female presented with convulsions and jaundice. She had subdural hematoma on neuroimaging and CPSS on Doppler. She responded to medical therapy but was subsequently lost to follow-up. A 1 day-old male with respiratory distress and pulmonary hypertension subsequently developed necrotizing enterocolitis was detected to have CPSS. He did not take treatment and left against medical advice.