Case report demonstrates improved cardiopulmonary function with the Wang procedure and Matrix-RIB bar in complex asphyxiating thoracic dysplasia.
Asphyxiating Thoracic Dysplasia (ATD), marked by chest wall depression and cardiopulmonary dysfunction, poses therapeutic challenges in secondary cases due to concurrent primary pathologies. This report details the Wang procedure with Matrix-RIB bar in a 66-year-old female with osteomalacia-induced secondary ATD. Prolonged prone positioning and glucocorticoid-induced osteoporosis led to bilateral rib fractures, severe chest wall collapse, and respiratory failure. Surgical correction involved rib osteotomy, preshaping, and fixation using the Wang procedure with Matrix-RIB bar to reconstruct the chest wall. Postoperatively, the patient transitioned to non-invasive ventilation with improved cardiopulmonary function. The Wang procedure demonstrates efficacy and safety in complex secondary ATD, particularly in osteomalacia-related cases, emphasising tailored surgical strategies for diverse etiologies. This approach enhances treatment outcomes, offering a valuable framework for similar cases.
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Zheng et al. (2025) studied this question.
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