Left Thoracic Kidney with Partially Intrathoracic Spleen with Diaphragmatic Defect- Rare Entity

Introduction: Intrathoracic kidney is a rare type of renal ectopia. Occurs due to congenital diaphragmatic defect which causes herniation of abdominal contents. Most common on left side and in male patient, usually asymptomatic.  Case Report: A 42-year-old male patient presented to our hospital with abdominal pain, CT scan of abdomen showing left side elevation of hemidiaphragm with intrathoracic kidney, spleen, tail of pancreas, splenic flexure. We have done exploratory laparotomy with reduction of intraperitoneal herniated contents with placation of left hemidiaphragm. Post follow up patient was stable.  Discussion: Renal ectopia is very rare findings usually found accidentally in radiological images or while doing thoracotomy.it occurs due to congenital or acquired causes. In acquired because it occurs due to injury to diaphragm. On congenital causes when there is delayed closure of diaphragm causes delaying in mesonephron closure leads to diaphragmatic hernia with intrathoracic kidney and other abdominal contents.  Conclusion: Intrathoracic kidney with spleen and other structures are very rare, accidental findings, most common due to congenital causes, in male patients and more in left side than in right side and usually patient have no any complain related to it.