Goldenhar Syndrome- No More a Challenge to Anaesthesiologist

A 17 year old patient, K/C/O Goldenhar syndrome came for right external ear reconstruction. Patient had typical features of the syndrome with hypoplastic mandible and maxilla, malocclusion of teeth, misaligned teeth, retrognathia and hypoplastic hyoid bone. Anticipating a difficult intubation it was decided to go ahead with awake intubation in this patient. Blind nasal intubation was planned because of non availability of fibreoptic in our institution and it was achieved with 7 mm ivory white north pole tube with dexmedetomidine infusion at rate of 0.5mcg/kg/hr and topical anesthesia.