Case report explores renal agenesis and seminal vesicle cyst in a young male, suggesting imaging aids diagnosis.
Background: Zinner Syndrome is a rare congenital condition of the male urogenital tract, defined by unilateral renal agenesis, ipsilateral seminal vesicle cyst, and ejaculatory duct obstruction, resulting from mesonephric duct maldevelopment. Case Presentation: A 27-year-old male presented with urinary frequency, dysuria, painful ejaculation, and secondary infertility. His history included recurrent urinary tract infections and a solitary kidney. Physical examination revealed a retrovesical mass. Imaging Findings: Transabdominal ultrasound identified a 5.5-cm left seminal vesicle cyst and absent left kidney. CT urogram confirmed renal agenesis and a non-enhancing retrovesical cyst. Pelvic MRI demonstrated a T1-hyperintense, T2-intermediate cyst with hemorrhagic contents, ejaculatory duct obstruction, and associated prostatitis. Conclusion: Multimodal imaging, particularly MRI, is essential for diagnosing Zinner Syndrome in young males with urogenital symptoms or infertility. Accurate radiological assessment guides management, ranging from conservative surveillance to surgical intervention.
No takes yet. Share an insight, caveat, or question.
Lekha et al. (2025) studied this question.
Synapse has enriched 5 closely related papers on similar clinical questions. Consider them for comparative context: