Primary Pulmonary Epithelioid Angiosarcoma Presenting in a 59-Year-Old Woman: A Report of a Rare Case

Primary pulmonary angiosarcomas are rare malignancies, with aggressive clinical behavior and poor prognosis. Here we present a case of a rare primary pulmonary epithelioid angiosarcoma in a 59-year-old woman who initially presented with right-sided chest pain and shortness of breath. Chest X-ray revealed right lower lobe atelectasis, while a chest computed tomography angiography (CTA) showed a large right hydrothorax with collapse of most of the right lung. A right lower lobe resection was performed and histologic and immunohistochemical analyses were consistent with a primary pulmonary epithelioid angiosarcoma. The patient was discharged, given supportive care, and died 12 days following her last operation.