Extraskeletal Myxoid chondrosarcoma (EMC) is a rare and aggressive soft tissue malignancy with a high risk of metastasis because it is radio-chemoresistant. The aim of this study is to describe the clinical evolution of this tumor after the detection of distant metastases and to schematize its metastatic evolution. This is a 26-year-old man, followed for more than 9 years in our institution for EMC of the right leg with synchronous pulmonary metastases, documented by medical imaging. Pathological analysis confirmed the diagnosis and the patient underwent surgical treatment (amputation) followed by adjuvant chemotherapy and follow-up revealed multiple metastases. The present case showed that EMC has the potential for a more invasive transition during its prolonged clinical course, which may lead to a poor prognosis. In addition, this work recommends that we consult a specialist in the event of the slightest swelling, however trivial, whatever the site, in order to clarify its histological nature thus avoiding unfortunate progression.
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G et al. (2024) studied this question.
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