A Case of Pheocromocytoma Arising From Heterotopic Adrenal Gland in Children

Pheochromocytoma is a rare tumor in children. We present the case of a 9-year-old female child with heterotopic retroperitoneal localized pheochromocytoma, clinically manifesting hypertension, tachycardia and headache. The diagnosis was based on abdominal ultrasound, CT and contrast-enhanced MRI, confirmed by evaluation of free plasma catecholamine metabolites and testing of fractionated urinary metanephrines. This case is of interest due to an atypical position and vascularization of the pheochromoctioma, located retroperitoneally on the right, casuistical described in the literature, which created some diagnostic confusions. The use of the transperitoneal approach, in this case, allowed an excellent exposure and radical removal of the tumor without injuring the kidney and ureter attached to the tumor.